Malignancy and Immune Disorders in Patients with Hereditary Angioedema

نویسندگان

چکیده

Hereditary angioedema (HAE) is well documented condition with inherited deficiency or dysfunction of C1 inhibitor. However, its association other immune disorders such as autoimmunity, malignancy and primary immunodeficiency not known.

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ژورنال

عنوان ژورنال: The Journal of Allergy and Clinical Immunology

سال: 2021

ISSN: ['1097-6825', '0091-6749', '1085-8725']

DOI: https://doi.org/10.1016/j.jaci.2020.12.121